Trigeminal neuralgia caused by an underlying disease other than those described above.
- Recurrent paroxysms of unilateral facial pain fulfilling criteria for 13.1.1 Trigeminal neuralgia, either purely paroxysmal or associated with concomitant continuous or near-continuous pain, but not necessarily unilateral
- Both of the following:
- a disorder other than those described above, but known to be able to cause trigeminal neuralgia, has been diagnosed1
- pain has developed after onset of the disorder, or led to its discovery
- Not better accounted for by another ICHD-3 diagnosis.
Recognized causes are skull-base bone deformity, connective tissue disease, arteriovenous malformation, dural arteriovenous fistula and genetic causes of neuropathy or nerve hyperexcitability.